← All hypotheses

Immune Response: Why Re-dosing Matters

PHARMACOKINETICS

AAV gene therapy is essentially one-shot. After the first dose, the immune system generates neutralizing antibodies (NAbs) against the viral capsid. These NAbs persist for years thanks to memory B cells. A second dose of the same serotype gets neutralized before it reaches target cells.

This is not a hypothetical concern. Patients seropositive for anti-AAV antibodies are excluded from most clinical trials. And 30-60% of the general population already has pre-existing anti-AAV immunity from childhood wild-type AAV exposure.

For STRC gene therapy, this creates a specific problem. If the first dose does not achieve sufficient transduction, there is no second chance with the same vector. This is where the delivery vehicle choice becomes critical.

NAb Kinetics After First Dose

Neutralizing antibody titer over time after intracochlear AAV administration (seronegative patient). Cochlear immune privilege reduces systemic response by ~30% compared to IV delivery.

Peak Peak: day 14, ~2.6× baseline
Mem. Memory B cells maintain 10% of peak titer indefinitely
Win. For seronegative patients with low baseline, re-dosing window may open within weeks. For seropositive patients (baseline titer ≥50): window opens at day 49 at earliest.

Seroprevalence Barrier

Percentage of population with pre-existing neutralizing antibodies by AAV serotype:

AAV1 67%
AAV2 72%
AAV5 40%
AAV8 38%
AAV9 47%
Anc80L65 20%

Pediatric (<5 years): 20-30% (lower than adults)

Boutin et al. 2010, Calcedo et al. 2015

Delivery Vehicle Comparison

Property AAV LNP Exosome
First-dose efficiency 60-90% 10-50% 5-20%
Immune response Strong: IgG NAbs + memory B cells Innate only (complement). No memory Minimal (autologous)
Re-dosing Extremely difficult (same serotype) Every 2-4 weeks Anytime
Seroprevalence barrier 30-60% excluded 0% 0%
Cochlear advantage Partial immune privilege Repeatable compensates lower per-dose Natural barrier crossing
Clinical readiness Phase 1/2 (for OTOF) Preclinical (cochlear), approved (COVID) Early research

What This Means for STRC

Single-vector mini-STRC has a higher probability of success on the first (and possibly only) AAV dose. Dual-vector full STRC wastes half the dose on each vector, then loses another 70-80% to failed recombination.

The hybrid strategy from our delivery model (AAV surgery for base coverage + LNP top-up via sonoporation) directly addresses the re-dosing problem. AAV provides high initial transduction. LNP provides indefinite maintenance doses without immune barrier.

For pediatric patients like Misha (age 4), anti-AAV seroprevalence is lower (20-30%). This is a timing advantage that diminishes with age as children encounter wild-type AAV.

🧮
Full model: NAb kinetics, seroprevalence, vehicle comparison
View on GitHub: immune_response_model.py

Cochlear immune privilege is real but incomplete. The blood-perilymph barrier is weaker than the blood-brain barrier. Local AAV delivery to the cochlea generates lower systemic NAb responses than intravenous delivery, but still sufficient to block re-dosing with the same serotype. The 30% reduction factor is estimated from comparative studies of intraocular vs systemic AAV delivery in NHPs (Timmers 2022). Direct cochlear NAb kinetics data in humans does not yet exist.

← All hypotheses